1.
Describe the embryology of the ear.
2.
Discuss the types of congenital malformations of the inner ear.
3.
Discuss the difference between atresia and microtia.
4.
What are the ear abnormalities seen in CHARGE syndrome?
5.
Discuss the Jahrsdorfer and De La Cruz classifications systems for grading aural atresia. Are there any absolute indications and contraindications for atresiaplasty?
6.
What are some congenital labyrinthine anomalies found in patients?
7.
What syndromes are associated with enlarged vestibular aqueduct syndrome?
8.
Describe the differences between Scheibe’s anomaly, Alexander aplasia, Mondini aplasia and Michel aplasia.
9.
What are the different types of microtia deformities? Incidence?
10.
What are some associated deformities in microtia patients?
11.
Describe the causes of hearing loss in Down syndrome patients.
12.
What is X-linked stapes gusher syndrome?
13.
Why do cholesteatomas form in congenital aural atresia?
14.
Describe vascular malformations of the ear such has high jugular bulb and aberrant carotid artery.
15.
Describe some common facial nerve abnormalities seen in atresia.
16.
Discuss the appropriate evaluation for the patient with unilateral microtia?
17.
What additional considerations need to be made in the case of bilateral microtia with complete aural atresia? What is the incidence of bilateral occurrence?
18.
What are the treatments, approaches, and time course of atresia repair.
19.
Discuss the rehabilitation options for unilateral microtia. Discuss the different surgical stages and their timing.
20.
What are the most common complications of microtia surgery?
21.
Are any congenital ear malformations associated with increased risk of meningitis?
22.
Can you perform a cochlear implant on a patient with an inner ear malformation? What might you need to consider?
23.
What are different ear malformations seen in congenital aural atresia?
Reference(s):
Dedhia, K., Yellon, R. F., Branstetter, B. F., & Egloff, A. M. (2012). Anatomic variants on computed tomography in congenital aural atresia. Otolaryngology–Head and Neck Surgery : Official Journal of American Academy of Otolaryngology-Head and Neck Surgery, 147(2), 323–328.